Episodic idiopathic systemic capillary leak syndrome in a girl.

[systemic capillary leak syndrome]

Episodic idiopathic systemic capillary leak syndrome is a rare disorder that presents with attacks of circulatory shock due to plasma leakage into the extravascular space . Reported here is the case of a girl who had recurrent circulatory shock . The diagnosis of episodic idiopathic systemic capillary leak syndrome was made following the fourth episode . The course was favorable following acute i .v . cristalloids and methylprednisolone .