Rare Diseases Symptoms Automatic Extraction

Systemic capillary leak syndrome: recognition prevents morbidity and mortality.

[systemic capillary leak syndrome]

Idiopathic systemic capillary leak syndrome (SCLS) is extremely rare but carries a high morbidity and mortality. The diagnosis is made clinically by a classic triad of hypotension, hypoalbuminaemia and haemoconcentration. There have been recent advances in understanding the pathophysiological basis for SCLS and in effective prophylaxis. We report a case of SCLS to increase awareness of the condition and to highlight the benefits of prophylactic intravenous immunoglobulin in this condition.

Diseases presenting "mortality" symptom

  • congenital diaphragmatic hernia
  • cushing syndrome
  • dystrophic epidermolysis bullosa
  • epidermolysis bullosa simplex
  • erdheim-chester disease
  • erythropoietic protoporphyria
  • heparin-induced thrombocytopenia
  • junctional epidermolysis bullosa
  • lamellar ichthyosis
  • legionellosis
  • locked-in syndrome
  • megacystis-microcolon-intestinal hypoperistalsis syndrome
  • oculocutaneous albinism
  • scrub typhus
  • systemic capillary leak syndrome
  • thoracic outlet syndrome
  • typhoid
  • von hippel-lindau disease

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