Rare Diseases Symptoms Automatic Extraction

Systemic capillary leak syndrome: recognition prevents morbidity and mortality.

[systemic capillary leak syndrome]

Idiopathic systemic capillary leak syndrome (SCLS) is extremely rare but carries a high morbidity and mortality. The diagnosis is made clinically by a classic triad of hypotension, hypoalbuminaemia and haemoconcentration. There have been recent advances in understanding the pathophysiological basis for SCLS and in effective prophylaxis. We report a case of SCLS to increase awareness of the condition and to highlight the benefits of prophylactic intravenous immunoglobulin in this condition.

Diseases presenting "hypotension" symptom

  • achondroplasia
  • adrenal incidentaloma
  • congenital adrenal hyperplasia
  • congenital diaphragmatic hernia
  • cutaneous mastocytosis
  • fabry disease
  • familial mediterranean fever
  • primary effusion lymphoma
  • scrub typhus
  • systemic capillary leak syndrome
  • thoracic outlet syndrome
  • typhoid

This symptom has already been validated