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Systemic capillary leak syndrome: recognition prevents morbidity and mortality.

[systemic capillary leak syndrome]

Idiopathic systemic capillary leak syndrome (SCLS) is extremely rare but carries a high morbidity and mortality. The diagnosis is made clinically by a classic triad of hypotension, hypoalbuminaemia and haemoconcentration. There have been recent advances in understanding the pathophysiological basis for SCLS and in effective prophylaxis. We report a case of SCLS to increase awareness of the condition and to highlight the benefits of prophylactic intravenous immunoglobulin in this condition.

Diseases presenting "been recent advances in understanding the pathophysiological basis" symptom

  • systemic capillary leak syndrome

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