Rare Diseases Symptoms Automatic Extraction
Home
A random Abstract
Our Project
Our Team
[Idiopathic capillary hyperpermeability syndrome revealing of Waldenström disease].
[systemic capillary leak syndrome]
Waldenstrom
disease
is
a
rare
hematologic
disorder
characterized
by
lymphoplasmacytic
proliferation
associated
with
the
production
of
monoclonal
IgM
.
Visceral
injuries
are
described
but
some
are
rare
(
lung
)
,
others
never
reported
(
cardiac
)
.
We
report
for
information
and
discussion
a
case
representing
these
particular
situations
,
considering
that
these
attacks
were
revealing
.
It
is
a
63
year
old
man
who
was
admitted
to
the
emergency
room
in
an
array
of
tamponade
,
with
edema
at
the
front
and
four
members
.
Clinical
and
radiological
examinations
were
objectified
bilateral
pleural
effusion
,
ascite
and
pericarditis
.
The
biological
exploration
showed
pancytopenia
,
serum
proteins
120
g
/
L
and
a
monoclonal
peak
migrant
beta
2
globulin
electrophoresis
which
is
made
by
monoclonal
immunoglobulin
M
(
IgM
kappa
)
.
The
bone
marrow
confirmed
the
diagnosis
of
the
Waldenström
disease
.
This
is
a
mode
of
revelation
never
described
before
.
Considering
this
case
,
it
would
be
wise
to
think
of
a
Waldenström
disease
before
any
polyserositis
.
Diseases
Validation
Diseases presenting
"pancytopenia"
symptom
familial mediterranean fever
homocystinuria without methylmalonic aciduria
oculocutaneous albinism
papillon-lefèvre syndrome
severe combined immunodeficiency
systemic capillary leak syndrome
This symptom has already been validated