Anaesthesiological considerations in patients with Sneddon's syndrome.

[sneddon syndrome]

Sneddon 's syndrome is a rare disease with strong gender prevalence of females . This syndrome is characterized by livedo racemosa and cerebrovascular lesions . Since no specific test is available , the clinical differentiation from other disorders with similar symptomatology may raise difficulties . The cerebral involvement includes strokes with cases of more than one ischaemic event having been reported . Associations with convulsions , heart valve disease , systemic hypertension , and renal impairment have been described . We report the case of a 5 -year -old boy who was anaesthesized for dental surgery . Due to the fact that 50 % of Sneddon 's syndrome patients develop mental retardation , even minor procedures require general anaesthesia . A review of the literature is added and specific anaesthesiological aspects of the perioperative care of Sneddon 's syndrome are discussed .