[Sneddon's syndrome: 4 cases and a review of the literature].

[sneddon syndrome]

Sneddon syndrome is an association of livedo racemosa and cerebrovascular ischemic events generally occurring in young adults . This is an uncommon chronic progressive arterio-occlusive disorder of unknown cause involving small and medium sized vessels . We report four cases . One case was disclosed by cerebral hemorrhage . One pathogenic hypothesis suggests the involvement of an idiopathic progressive inflammatory arteriopathy or secondary thrombotic disorder comparable with antiphospholipid syndrome .