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Infarction of the right hemisphere in a patient with antiphospholipid antibody syndrome.
[sneddon syndrome]
Hemicraniectomy
as
a
surgical
treatment
for
intracranial
pressure
following
large
ischemic
lesions
is
widely
practiced
in
selected
patients
.
The
antiphospholipid
antibody
syndrome
(
APS
)
,
a
disorder
characterized
by
recurrent
arterial
and
venous
thrombosis
,
is
a
very
rare
cause
of
space
occupying
ischemic
lesions
.
We
present
a
case
of
a
35
year
old
female
diagnosed
with
APS
who
initially
presented
with
small
ischemic
lesions
and
within
days
developed
a
massive
near-
total
infarction
of
the
right
hemisphere
.
Because
of
central
nervous
system
,
skin
and
systemic
manifestations
Sneddon
's
syndrome
and
catastrophic
antiphospholipid
antibody
syndrome
(
CAPS
)
remained
a
possible
diagnoses
.
Sneddon
's
syndrome
is
a
non-
inflammatory
occlusive
arteriopathy
of
small
and
medium
size
arteries
predominantly
of
the
skin
and
brain
,
whereas
the
catastrophic
antiphospholipid
antibody
syndrome
is
characterized
by
acute
multi-organ
system
thrombosis
of
small
and
large
vessels
.
In
addition
to
the
diagnostic
criteria
for
APS
a
heterozygous
factor
V
Leiden
mutation
was
found
in
this
patient
,
which
may
be
a
contributing
risk
factor
for
cerebral
ischemia
.
When
considering
invasive
decompressive
procedures
the
neurosurgeon
has
to
be
aware
of
the
poor
prognosis
of
some
forms
of
APS
with
systemic
manifestations
.
Diseases
Validation
Diseases presenting
"intracranial pressure"
symptom
achondroplasia
alexander disease
hydrocephalus with stenosis of the aqueduct of sylvius
sneddon syndrome
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