[Sneddon syndrome: a rare cause of vascular dementia].

[sneddon syndrome]

Few vascular dementias are diagnosed in memory clinic consultations . One type , a rare etiology , Sneddon syndrome , can lead patients to consult for an isolated memory complaint . We report the cases of two patients , aged 63 and 66 years , who presented frontocortical cognitive profile and behavior disorders . Seronegative Sneddon syndrome , complicated with dementia , was diagnosed in each case by noticing an association between , on MRI , an atrophy and several ischemic cerebrovascular accident aftermaths , and a livedo racemosa . Management of vascular risks factors improves the prognosis .

Diseases
Validation

Diseases presenting "dementia" symptom

adrenomyeloneuropathy

alexander disease

cadasil

canavan disease

carcinoma of the gallbladder

cushing syndrome

gm1 gangliosidosis

hereditary cerebral hemorrhage with amyloidosis

homocystinuria without methylmalonic aciduria

hydrocephalus with stenosis of the aqueduct of sylvius

inclusion body myositis

phenylketonuria

sneddon syndrome

x-linked adrenoleukodystrophy

This symptom has already been validated