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Anesthesia in a child with pyruvate dehydrogenase deficiency: a case report.
[pyruvate dehydrogenase deficiency]
We
report
a
case
in
a
pediatric
patient
with
pyruvate
dehydrogenase
deficiency
who
presented
for
a
left
foot
tendon
transfer
with
an
Achilles
tendon
lengthening
secondary
to
left
ankle
equinus
.
The
pathophysiology
of
pyruvate
dehydrogenase
deficiency
is
discussed
as
well
as
anesthetic
management
in
patients
with
pyruvate
dehydrogenase
deficiency
.