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Anesthesia in a child with pyruvate dehydrogenase deficiency: a case report.

[pyruvate dehydrogenase deficiency]

We report a case in a pediatric patient with pyruvate dehydrogenase deficiency who presented for a left foot tendon transfer with an Achilles tendon lengthening secondary to left ankle equinus. The pathophysiology of pyruvate dehydrogenase deficiency is discussed as well as anesthetic management in patients with pyruvate dehydrogenase deficiency.