Macrodactyly with skin hypertrophy: a minimal form of the Proteus syndrome.

[proteus syndrome]

The Proteus syndrome was described 1983 . It has asymmetric gigantism of the limbs , verrucous epidermal naevi , cerebriform enlargement of the plantar region , vascular malformations and neoplasms , as lipomas . It received this denomination after Proteus from the Greek mythology , who had the ability to change his form . A 15 year -old boy , reported a congenital hypertrophy with syndactily of the second and third right fingers . The second case is a 35 year -old man , who reported that since birth the second right toe was bigger than the other toes , skin hypertrophy was also observed . These cases document a localized form if the Proteus syndrome , which may widen the spectrum of its variability .