Soft-tissue necrosis complicating tibial osteotomy in a child with Proteus syndrome.

[proteus syndrome]

Proteus syndrome is a rare congenital hamartomatous disease frequently responsible for musculoskeletal deformities . The results and complications of surgical treatment are not well documented owing to the scarcity of reported cases .The authors report a case of poor evolution of valgus proximal tibial osteotomy in a 6 -year -old girl with Proteus syndrome . The surgery was complicated by extensive deep wound necrosis exposing the tibial bone , necessitating surgical excision , antibiotherapy and controlled wound healing . At 1 year postoperatively , the deformity recurred .The possibility of serious wound complications and of recurrence must be kept in mind when operating on a limb deformity in patients with Proteus syndrome . Potential complications should be taken into account in selecting the surgical correction technique : epiphysiodesis may be preferable to osteotomy .