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Combined liver and kidney transplantation in primary hyperoxaluria: a report of three cases and review of the literature.
[primary hyperoxaluria type 1]
Primary
hyperoxaluria
type
-
1
(
PH-
1
)
is
a
rare
autosomal
recessive
metabolic
disorder
leading
to
excessive
oxalate
production
,
deposition
of
calcium
oxalate
crystals
in
the
kidney
,
nephrocalcinosis
,
progressive
renal
failure
and
systemic
deposition
of
oxalate
(
oxalosis
)
.
Combined
liver
and
kidney
transplantation
(
LKT
)
,
which
has
been
accepted
as
the
treatment
of
choice
for
PH-
1
,
has
considerably
improved
patient
and
graft
survival
.
Herein
,
we
report
our
experience
of
three
children
with
PH-
1
who
underwent
combined
LKT
,
with
a
review
of
the
literature
.