Rare Diseases Symptoms Automatic Extraction
Home
A random Abstract
Our Project
Our Team
Primary effusion lymphoma.
[primary effusion lymphoma]
Primary
effusion
lymphoma
is
a
large
cell
non-
Hodgkin
lymphoma
localized
predominantly
in
body
cavities
and
occasionally
in
extracavitary
regions
.
It
presents
with
characteristic
lymphomatous
effusions
in
the
absence
of
solid
tumor
masses
,
and
pleural
,
peritoneal
,
and
pericardial
spaces
are
most
often
involved
.
It
is
typically
associated
with
human
herpesvirus
8
infection
in
immunocompromised
individuals
,
in
the
setting
of
human
immunodeficiency
virus
infection
,
organ
transplantation
,
or
in
rare
cases
advanced
age
.
Histologically
,
primary
effusion
lymphoma
is
characterized
by
atypical
lymphoid
cells
of
B-
cell
lineage
with
large
nuclei
and
prominent
nucleoli
.
Demonstration
of
human
herpesvirus
8
latent
antigens
is
required
for
diagnosis
,
and
treatment
modalities
are
limited
at
this
time
.
In
this
review
,
we
aim
to
summarize
clinicopathologic
features
of
this
rare
and
unique
entity
.
Diseases
Validation
Diseases presenting
"immunodeficiency"
symptom
adrenal incidentaloma
allergic bronchopulmonary aspergillosis
cushing syndrome
dracunculiasis
hirschsprung disease
hodgkin lymphoma, classical
homocystinuria without methylmalonic aciduria
kabuki syndrome
legionellosis
malignant atrophic papulosis
oculocutaneous albinism
omenn syndrome
papillon-lefèvre syndrome
primary effusion lymphoma
primary hyperoxaluria type 1
pyomyositis
severe combined immunodeficiency
sneddon syndrome
werner syndrome
wiskott-aldrich syndrome
wolf-hirschhorn syndrome
x-linked adrenoleukodystrophy
This symptom has already been validated