Targeting specific nutrient deficiencies in protein-restricted diets: some practical facts in PKU dietary management.

[phenylketonuria]

Among aminoacidopathies , phenylketonuria (PKU ) is the most prevalent one . Early diagnosis in the neonatal period with a prompt nutritional therapy (low natural-protein and phenylalanine diet , supplemented with phenylalanine-free amino acid mixtures and special low -protein foods ) remains the mainstay of the treatment . Data considering nutrient contents of cooked dishes is lacking . In this study , fourteen dishes specifically prepared for PKU individuals were analysed , regarding the lipid profile and iron and zinc contents . These dishes are poor sources of essential nutrients like Fe , Zn or n-3 fatty acids , reinforcing the need for adequate supplementation to cover individual patients ' needs . This study can contribute to a more accurate adjustment of PKU diets and supplementation in order to prevent eventual nutritional deficiencies . This study contributes to a better understanding of nutrient intake from PKU patients ' meals , showing the need for dietary supplementation .

Diseases
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Diseases presenting "poor sources" symptom

phenylketonuria

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