Papillon-Lefevre syndrome with pseudoainhum.

[papillon-lefèvre syndrome]

An interesting episode of Papillon-Lefevre syndrome in a 25 -year -old female with diffuse palmoplantar keratoderma , periodontitis and pseudoainhum of the toes is reported for academic interest . Her skin lesions improved with topical keratolytics and oral retinoid (acitretin ) whereas periodontic problems showed significant improvement with systemic antibiotics and proper implementation of oral hygienic measures . She is undergoing oral rehabilitation with orthodontic surgical procedures .