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Evaluation of two siblings with Papillon-Lefèvre syndrome 5 years after treatment of periodontitis in primary and mixed dentition.
[papillon-lefèvre syndrome]
This
case
report
describes
the
clinical
and
microbiologic
long
-term
outcome
5
years
after
periodontal
therapy
of
two
siblings
diagnosed
with
Papillon-
Lefèvre
syndrome
(
PLS
)
and
tinea
capitis
.
In
2005
,
two
brothers
diagnosed
with
PLS
and
tinea
capitis
began
periodontal
treatment
.
Both
of
them
showed
premature
mobility
of
the
primary
dentition
,
markedly
increased
probing
depths
,
and
subgingival
Aggregatibacter
actinomycetemcomitans
(
previously
Actinobacillus
actinomycetemcomitans
;
Aa
)
.
Initial
therapy
consisted
of
scaling
and
root
planing
based
on
the
concept
of
full-mouth
disinfection
,
extraction
of
periodontally
hopeless
deciduous
teeth
,
and
systemic
antibiotics
.
Reevaluation
of
clinical
parameters
revealed
a
dramatic
improvement
.
After
that
,
the
patients
were
enrolled
in
a
stringent
maintenance
program
.
Microbiologic
monitoring
was
performed
1
and
5
years
after
treatment
.
Five
years
after
initial
treatment
,
the
periodontal
situation
was
stable
in
both
patients
.
Residual
deciduous
teeth
,
with
the
exception
of
one
tooth
,
could
be
retained
and
no
further
teeth
were
lost
.
Further
disease
progression
on
the
previously
involved
teeth
was
controlled
,
and
development
of
periodontitis
on
erupting
teeth
was
prevented
for
a
period
of
5
years
.
Even
periodontally
affected
deciduous
teeth
can
be
treated
successfully
in
patients
with
PLS
.
Suppression
of
Aa
and
a
stringent
maintenance
program
are
of
high
importance
.
Diseases
Validation
Diseases presenting
"premature mobility of the primary dentition"
symptom
papillon-lefèvre syndrome
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