Rare Diseases Symptoms Automatic Extraction

The prosthodontic management of a young edentulous patient with the papillon lefevre syndrome-a rare case report.

[papillon-lefèvre syndrome]

The Papillon Lefevre syndrome is an autosomal recessive disorder which is characterized by various dermatological manifestations and periodontitis as a manifestation of a systemic disease. Its aetiopathogenesis is thought to be secondary to the mutation of the Cathepsin C gene. Various studies have shown that the immune related cells like the polymorphonuclear leucocytes and the macrophages and their precursors were affected.This report elicits about an edentulous male with this syndrome, who was treated with a modified complete denture prosthesis (hollow, maxillary, complete denture), considering his young age and low socioeconomic status.

Diseases presenting "periodontitis as a manifestation of a systemic disease" symptom

  • papillon-lefèvre syndrome

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