Megacystis microcolon intestinal hypoperistalsis syndrome.

[megacystis-microcolon-intestinal hypoperistalsis syndrome]

Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS ) is a multisystemic disorder in which impaired intestinal motor activity causes recurrent symptoms of intestinal obstruction in the absence of mechanical occlusion , associated with bladder distention without distal obstruction of the urinary tract . MMIHS and prune belly syndrome may overlap in most of the clinical features and discrimination of these two entities is important because the prognosis , management and consulting with parents are completely different . MMIHS outcome is very poor and in this article we present two neonates with MMIHS that both died in a few days .