Prominent Degos-like skin lesions in a patient with chronic cutaneous lupus erythematosus.

[malignant atrophic papulosis]

Malignant atrophic papulosis , commonly known as Degos disease , is a rare vasculopathy encompassing both benign , cutaneous and lethal systemic variants . We report a case of chronic cutaneous lupus erythematosus in a 41 -year -old male presenting with prominent Degos-like skin lesions . Multiple atrophic , porcelain-white , scar-like papules and plaques with dusky , erythematous borders , suggestive of malignant atrophic papulosis , were noted on the patient 's back . Additional cutaneous findings included photo-distributed facial erythema and discoid lupus-like plaques on the face , shoulders , and arms . Clinicopathological correlation supported a diagnosis of chronic cutaneous lupus erythematosus ; hydroxychloroquine was initiated with good clinical response . No new or active lesions were observed at the sixteen -month follow-up . This case highlights a rare skin finding associated with chronic cutaneous lupus erythematosus and underscores the importance of ruling out primary autoimmune disease , particularly lupus , before a diagnosis of malignant atrophic papulosis can be made .

Diseases
Validation

Diseases presenting "skin lesions" symptom

child syndrome

cowden syndrome

cutaneous mastocytosis

cystinuria

dystrophic epidermolysis bullosa

epidermolysis bullosa simplex

erdheim-chester disease

erythropoietic protoporphyria

familial mediterranean fever

focal myositis

gm1 gangliosidosis

heparin-induced thrombocytopenia

hirschsprung disease

junctional epidermolysis bullosa

lamellar ichthyosis

liposarcoma

lymphangioleiomyomatosis

malignant atrophic papulosis

oligodontia

omenn syndrome

papillon-lefèvre syndrome

primary effusion lymphoma

proteus syndrome

severe combined immunodeficiency

sneddon syndrome

waldenström macroglobulinemia

werner syndrome

wiskott-aldrich syndrome

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