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Prominent Degos-like skin lesions in a patient with chronic cutaneous lupus erythematosus.
[malignant atrophic papulosis]
Malignant
atrophic
papulosis
,
commonly
known
as
Degos
disease
,
is
a
rare
vasculopathy
encompassing
both
benign
,
cutaneous
and
lethal
systemic
variants
.
We
report
a
case
of
chronic
cutaneous
lupus
erythematosus
in
a
41
-
year
-old
male
presenting
with
prominent
Degos-like
skin
lesions
.
Multiple
atrophic
,
porcelain-
white
,
scar-like
papules
and
plaques
with
dusky
,
erythematous
borders
,
suggestive
of
malignant
atrophic
papulosis
,
were
noted
on
the
patient
's
back
.
Additional
cutaneous
findings
included
photo-distributed
facial
erythema
and
discoid
lupus-like
plaques
on
the
face
,
shoulders
,
and
arms
.
Clinicopathological
correlation
supported
a
diagnosis
of
chronic
cutaneous
lupus
erythematosus
;
hydroxychloroquine
was
initiated
with
good
clinical
response
.
No
new
or
active
lesions
were
observed
at
the
sixteen
-
month
follow-up
.
This
case
highlights
a
rare
skin
finding
associated
with
chronic
cutaneous
lupus
erythematosus
and
underscores
the
importance
of
ruling
out
primary
autoimmune
disease
,
particularly
lupus
,
before
a
diagnosis
of
malignant
atrophic
papulosis
can
be
made
.
Diseases
Validation
Diseases presenting
"good clinical response"
symptom
malignant atrophic papulosis
omenn syndrome
thoracic outlet syndrome
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