Malignant atrophic papulosis with severe gastrointestinal perforation and omental necrosis: a case report.

[malignant atrophic papulosis]

Malignant atrophic papulosis (MAP ) is a rare disease with an extremely grim prognosis , death being due to gastrointestinal perforation and neurological disorders . We report a severe case of MAP in a 37 -year old woman . The patient had three emergent laparotomies in 3 months for recurrent acute peritonitis due to omental thrombosis resulting in necrosis , multiple intestinal and mesenteric lesions , and severe gastrointestinal perforations . Multiple papular skin lesions were present for 1 year prior to surgery . Pathological findings revealed MAP . Surgical intervention was successful and the patient recovered smoothly but later died of malnutrition and septicaemia .

Diseases
Validation

Diseases presenting "skin lesions" symptom

child syndrome

cowden syndrome

cutaneous mastocytosis

cystinuria

dystrophic epidermolysis bullosa

epidermolysis bullosa simplex

erdheim-chester disease

erythropoietic protoporphyria

familial mediterranean fever

focal myositis

gm1 gangliosidosis

heparin-induced thrombocytopenia

hirschsprung disease

junctional epidermolysis bullosa

lamellar ichthyosis

liposarcoma

lymphangioleiomyomatosis

malignant atrophic papulosis

oligodontia

omenn syndrome

papillon-lefèvre syndrome

primary effusion lymphoma

proteus syndrome

severe combined immunodeficiency

sneddon syndrome

waldenström macroglobulinemia

werner syndrome

wiskott-aldrich syndrome

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