Malignant atrophic papulosis with severe gastrointestinal perforation and omental necrosis: a case report.

[malignant atrophic papulosis]

Malignant atrophic papulosis (MAP ) is a rare disease with an extremely grim prognosis , death being due to gastrointestinal perforation and neurological disorders . We report a severe case of MAP in a 37 -year old woman . The patient had three emergent laparotomies in 3 months for recurrent acute peritonitis due to omental thrombosis resulting in necrosis , multiple intestinal and mesenteric lesions , and severe gastrointestinal perforations . Multiple papular skin lesions were present for 1 year prior to surgery . Pathological findings revealed MAP . Surgical intervention was successful and the patient recovered smoothly but later died of malnutrition and septicaemia .