Rare Diseases Symptoms Automatic Extraction

Malignant atrophic papulosis: a case report with severe visual and neurological impairment.

[malignant atrophic papulosis]

Malignant atrophic papulosis, or Degos' disease, is a severe systemic vasculopathy extremely rare in children. The skin, gastrointestinal tract, and central nervous system are most frequently affected. We report a 5-year-old girl with malignant atrophic papulosis who presented with widespread skin lesions from early infancy and severe visual and neurological impairment.

Diseases presenting "and central nervous system are most frequently affected" symptom

  • malignant atrophic papulosis

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