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Renal angiomyolipoma and lymphangioleiomyomatosis in pregnancy.
[lymphangioleiomyomatosis]
This
is
a
literature
review
for
management
of
angiomyolipoma
(
AML
)
,
lymphangioleiomyomatosis
(
LAM
)
and
tuberous
sclerosis
(
TS
)
during
pregnancy
,
prompted
by
a
case
of
a
23
-
year
-old
woman
who
presented
with
generalised
itching
at
31
weeks
'
gestation
and
was
found
to
have
a
large
vascular
retroperitoneal
mass
in
the
lower
pole
of
the
left
kidney
.
Magnetic
resonance
imaging
(
MRI
)
was
suggestive
of
angiomyolipoma
with
multiple
large
aneurysms
and
haemorrhage
within
the
tumour
.
She
was
delivered
at
38
weeks
by
elective
caesarean
section
,
to
avoid
the
risk
of
rupture
and
bleeding
from
the
aneurysms
during
labour
.
Further
imaging
,
with
MR
angiogram
,
computed
tomography
(
CT
)
of
the
abdomen
and
pelvis
and
high
resolution
CT
(
HRCT
)
of
the
chest
,
confirmed
lymphangioleiomyomatosis
with
left
AML
.
She
had
embolisation
of
the
AML
performed
twice
,
8
weeks
apart
after
delivery
and
subsequently
had
a
left
nephrectomy
.
