Perineal lipoblastoma: a case report and review of literature.

[liposarcoma]

Lipoblastoma is a rare benign mesenchymal tumor that composes of embryonal white fat tissue and typically occurs in infants or young children under 3 years of age . It usually affects the extremities , trunk , head , and neck . The perineum is a rare location with only 7 cases reported in the literature . We describe a case of 3 -year -old girl with a lipoblastoma arising from perineum . An approximately 4 .5 cm × 3 .5 cm × 2 .5 cm nodule was resected in left perineum with satisfied results . Pathological examination showed that it was composed of small lobules of mature and immature fat cells , separated by fibrous septa containing small dilated blood vessels . The left perineal lipoblastoma , although rare , should be differentiated from some other mesenchymal tumors with similar histologic and cytological features .