Kindler syndrome: a rare cause of desquamative lesions of the gingiva.

[kindler syndrome]

Kindler syndrome is a rare syndrome with cutaneous and intraoral manifestations . It has been suggested that there is an overlap between this syndrome and another called Weary syndrome . Only 68 cases of Weary and Kindler syndromes have been reported , with fewer solely attributed to Kindler syndrome . The salient cutaneous features are neonatal bullae , poikiloderma , photosensitivity , and acral atrophy . This article presents the clinical intraoral findings of two siblings of consanguineous descent diagnosed as having Kindler syndrome . Both had an erythematous and erosive appearance of the gingiva ; one sibling had poor oral hygiene and a rapidly progressive form of periodontal disease ; the other , whose oral hygiene was acceptable , had no detectable bone loss .