Pyloric atresia-Three cases and review of literature.

[junctional epidermolysis bullosa]

Pyloric atresia (PA ) is a rare congenital anomaly that constitutes approximately 1 % of all intestinal atresias , and its incidence is approximately 1 in 100 ,000 live births . PA may occur as an isolated condition or associated with other abnormalities , the most common being Junctional epidermolysis bullosa (JEB ). Evidence suggests that PA -EB (Pyloric Atresia - Epidermolysis Bullosa ) Syndrome is a distinct entity . In this report , we present three cases of pyloric atresia , one of which was associated with Junctional epidermolysis bullosa . The literature on the subject is also reviewed .