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Sporadic inclusion body myositis presenting with severe camptocormia.
[inclusion body myositis]
Sporadic
inclusion
body
myositis
(
sIBM
)
is
a
slowly
progressive
idiopathic
inflammatory
myopathy
.
The
characteristic
early
quadriceps
and
finger
flexor
muscle
weakness
often
leads
to
the
diagnosis
of
sIBM
,
especially
when
all
canonical
pathological
features
of
sIBM
are
not
present
on
muscle
biopsy
.
Weakness
of
the
paraspinal
muscles
,
resulting
in
head
drop
and
/
or
camptocormia
,
is
a
rare
clinical
finding
along
the
course
of
sIBM
,
and
even
more
rare
as
the
presenting
feature
.
We
describe
two
patients
with
sIBM
manifesting
with
camptocormia
as
the
sole
clinical
manifestation
for
several
years
prior
to
the
diagnosis
by
muscle
biopsy
.
This
observation
emphasizes
the
role
of
sIBM
in
the
etiology
of
camptocormia
and
the
need
to
consider
this
common
myopathy
as
a
cause
of
weakness
,
despite
the
lack
of
classic
quadriceps
and
finger
flexor
muscle
weakness
years
after
the
onset
of
the
paraspinal
muscle
weakness
.
Diseases
Validation
Diseases presenting
"camptocormia"
symptom
focal myositis
inclusion body myositis
This symptom has already been validated
