Hereditary hypohidrotic ectodermal dysplasia: report of a rare case.

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Hereditary Hypohidrotic Ectodermal Dysplasia (HHED ), an X-linked , recessive , Mendelian character , is seen usually in males and it is inherited through female carriers . It is characterised by congenital dysplasia of one or more ectodermal structures and it is manifested by hypohidrosis , hypotrichosis and hypodontia . It results from abnormal morphogenesis of cutaneous and oral embryonic ectoderm . Here , we are presenting a rare case of HHED in a 19 year female with classic features of this condition .