Unilateral segmentally arranged basaloid follicular hamartomas with osteoma cutis and hypodontia: a case of Happle-Tinschert syndrome.

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Happle-Tinschert syndrome (HTS ) is a rare syndrome characterized by segmentally arranged basaloid follicular hamartomas (BFH ) associated with ipsilateral osseous , dental and cerebral abnormalities . Happle and Tinschert first reported this disorder in 2008 , and three cases with similar presentations have since been reported . We report another case , that of a 40 -year -old man , presenting with the characteristic clinical features of HTS .