Rare Diseases Symptoms Automatic Extraction
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A random Abstract
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Death in consequence of late failure of endoscopic third ventriculostomy.
[hydrocephalus with stenosis of the aqueduct of sylvius]
Late
failure
of
originally
successful
endoscopic
third
ventriculostomy
(
ETV
)
is
considerably
less
common
than
failure
of
ventriculo-peritoneal
(
V-P
)
shunt
in
treatment
of
hydrocephalus
.
Death
in
consequence
of
late
ETV
failure
is
a
very
rare
complication
,
so
far
having
been
mentioned
in
literature
in
13
patients
only
.
We
present
the
case
of
an
11
-
year
-old
girl
who
died
in
consequence
of
ETV
failure
26
months
after
the
endoscopic
procedure
.
Histopathology
proved
the
closure
of
stoma
by
gliotic
tissue
.
We
can
assume
that
reduced
compliance
of
the
ventricular
wall
in
long
-term
V-P
shunt
,
aqueductal
stenosis
as
a
cause
of
hydrocephalus
as
well
as
rapid
onset
of
clinical
symptoms
prior
to
ETV
might
be
the
cause
of
acute
onset
of
intracranial
hypertension
after
late
ETV
failure
.
Potential
prevention
of
sudden
death
seems
to
be
the
implantation
of
subcutaneous
reservoir
during
the
endoscopic
procedure
,
which
allows
simple
and
rapid
reduction
of
intraventricular
pressure
.
Diseases
Validation
Diseases presenting
"intracranial hypertension"
symptom
achondroplasia
cushing syndrome
hydrocephalus with stenosis of the aqueduct of sylvius
von hippel-lindau disease
This symptom has already been validated