Rare Diseases Symptoms Automatic Extraction
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A fluorescent probe for GM1 gangliosidosis related β-galactosidase: N-(dansylamino)hexylaminocarbonylpentyl-1,5-dideoxy-1,5-imino-D-galactitol.
[gm1 gangliosidosis]
N-
(
Dansylamino
)
hexylaminocarbonylpentyl-
1
,
5
-
dideoxy-
1
,
5
-
imino-
D-
galactitol
,
a
strong
competitive
inhibitor
of
β-galactosidase
,
enhances
residual
β-galactosidase
activities
in
fibroblasts
and
serves
as
lead
en
route
to
diagnostic
compounds
for
tracking
the
fate
of
mutant
β-gal
as
well
as
aberrant
GM
1
gangliosides
by
live
cell
imaging
.
