[The rupture of splenic artery aneurysm in Erdheim disease].

[erdheim-chester disease]

Splenic vessel aneurysm is often a casual pathology during strumental imaging or laparotomy . The first cause for the formation of the aneurysm is a vessel primitive degenerative pathology of the medium wall , or idiopathic cystic medionecrosis , that to develop in aneurysmatic dissection . In the early diagnosis , in the selective patients , resulted indicate an endovascular therapy , while in emergency the laparotomy is a gold strandard for reduction morbility and mortality . In this paper , the Authors described a rare case of rupture of the lienal vessel aneurysm in Erdheim disease , and reported clinical features , indications and procedures for better treatment .