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[Erdheim-Chester disease: report of a case and literature review].
[erdheim-chester disease]
The
Erdheim-
Chester
disease
is
a
rare
non-
Langerhans
hystiocytose
acquired
in
adults
.
It
results
from
a
xanthogranulomatous
infiltration
,
consists
of
histioccytes
foamy
and
is
characterized
by
heterogeneous
systemic
manifestations
.
The
most
frequent
clinical
manifestations
of
the
disease
are
the
bone
with
a
long
bone
uptake
on
bone
scintigraphy
99
Tc
(
Dion
et
al
.
,
2006
)
and
urological
damage
with
an
array
of
pseudo
retroperitoneal
fibrosis
.
We
report
the
case
of
a
64
-
year
-old
man
in
whom
was
founded
in
the
course
of
acute
obstructive
renal
disease
with
Erdheim-
Chester
pseudofibrose
retroperitoneal
.
