Rare Diseases Symptoms Automatic Extraction
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A random Abstract
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Immunopathological analysis of Erdheim-Chester disease with massive ascites.
[erdheim-chester disease]
We
treated
a
77
-
year
-old
woman
with
pleural
and
pericardial
effusion
and
ascites
.
Initially
,
collagen
vascular
disease
was
suspected
due
to
the
presence
of
anti-centromere
antibodies
and
suspected
complication
of
pulmonary
arterial
hypertension
.
However
,
soft
-tissue
abnormalities
surrounding
the
bilateral
kidneys
detected
on
computed
tomography
(
CT
)
and
symmetrical
lesions
of
the
long
bones
detected
on
bone
scintigraphy
made
us
consider
a
diagnosis
of
Erdheim-
Chester
disease
(
ECD
)
,
which
is
a
rare
form
of
histiocytosis
.
We
immunochemically
analyzed
the
cells
derived
from
the
ascites
in
detail
and
confirmed
the
diagnosis
.
Immunocytochemical
analyses
may
therefore
help
to
achieve
a
better
understanding
of
the
pathogenesis
of
this
rare
disease
.
