Dystrophic epidermolysis bullosa in a child.

[dystrophic epidermolysis bullosa]

Epidermolysis Bullosa (EB ) is a form of severe skin adhesion defect due to the disruption of the dermal- epidermal junction . It is classified into simplex and dystrophic forms depending on the level at which the junction is compromised . Repeated ulcerations and bullae formation in the mouth lead to scarring that brings about various changes in the oral cavity . These include loss of sulcular depth , ankyloglossia , limited mouth opening and other dentoalveolar changes . At present while there is no cure for EB , the therapeutic approaches are essentially aimed at controlling the infections and maintaining an acceptable quality of life . Dental management should aim at maintaining a functional dentition that would help in mastication and favour nutrition . Oral manifestations and dental management in a child diagnosed with dystrophic EB since birth are presented here .

Diseases
Validation

Diseases presenting "oral manifestations" symptom

cowden syndrome

dentinogenesis imperfecta

dystrophic epidermolysis bullosa

kabuki syndrome

oligodontia

oral submucous fibrosis

proteus syndrome

triple a syndrome

zellweger syndrome

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