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Fluoroscopically guided dilation of esophageal strictures in patients with dystrophic epidermolysis bullosa: long-term results.
[dystrophic epidermolysis bullosa]
The
purpose
of
this
study
was
to
investigate
the
immediate
and
long
-term
outcomes
after
fluoroscopically
guided
balloon
dilation
of
esophageal
strictures
in
a
series
of
patients
with
dystrophic
epidermolysis
bullosa
(
DEB
)
.
Between
2005
and
2011
,
the
medical
records
of
all
patients
with
DEB
treated
with
fluoroscopically
guided
balloon
dilation
of
esophageal
strictures
were
included
in
the
study
and
retrospectively
analyzed
.
The
indication
for
treatment
was
dysphagia
attributed
to
at
least
one
radiologically
verified
esophageal
stricture
.
The
primary
endpoints
of
the
study
included
procedural
technical
success
,
clinical
improvement
assessed
with
a
0
-
4
dysphagia
score
,
and
major
complication
rate
.
Secondary
endpoints
were
patient
survival
and
reintervention
rates
.
Nineteen
consecutively
registered
patients
with
DEB
(
age
range
,
10
-
51
years
;
mean
,
30
±
12
.
2
years
)
and
dysphagia
due
to
esophageal
strictures
were
treated
with
fluoroscopically
guided
balloon
dilation
.
In
total
,
90
procedures
and
121
dilations
were
performed
to
manage
28
lesions
.
Balloon
diameter
ranged
from
8
to
18
mm
.
The
mean
follow-up
time
was
47
.
51
±
16
.
64
months
(
range
,
17
-
73
months
)
.
The
technical
success
rate
was
96
.
7
%
(
87
/
90
)
.
There
were
no
major
complications
.
The
mean
reintervention
rate
was
1
.
19
dilations
per
patient
per
year
,
and
the
postprocedural
dysphagia
score
(
0
.
72
[
95
%
CI
,
0
.
56
-
0
.
87
]
)
was
significantly
lower
than
baseline
(
2
.
50
[
95
%
CI
2
.
35
-
2
.
65
]
)
(
p
<
0
.
001
)
.
Repeated
fluoroscopically
guided
balloon
dilation
is
safe
and
effective
for
the
management
of
dysphagia
caused
by
esophageal
strictures
in
DEB
.
Use
of
this
technique
was
associated
with
marked
clinical
improvement
in
dysphagia
and
satisfactory
long
-term
reintervention
rates
with
no
major
complications
.
Diseases
Validation
Diseases presenting
"consecutively registered patients"
symptom
dystrophic epidermolysis bullosa
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