Rare Diseases Symptoms Automatic Extraction

[Pedigree analysis and prosthodontic treatment of patients with dentinogenesis imperfecta type II].

[dentinogenesis imperfecta]

To study the heritable character and explore the prosthodontic treatment of opalescent dentin, also known as dentinogenesis imperfecta type II(DGI-II).Pedigree analysis was performed in the family members of patients with DGI-II found in Shanghai. The proband was treated with ceramometal restorations and investigated the treatment status of the DGI-II affected individuals in the family.Five sequential generations with DGI-II were found in this family. The prevalence of later generation was approximately 50%. The rate of prosthodontic treatment was 90% nearly, including ceramometal restorations in the most of the patients and removable partial dentures in the others. The esthetic and mastication functions of the patients were good after treatment.DGI-II showed a autosomal dominant pattern of inheritance. Ceramaometal restorations can prevent the affected teeth from abrasive and fracture, and also can help rehabilitate the esthetic and mastication functions of the teeth.