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Spectrum of dentin dysplasia in a family: case report and literature review.
[dentin dysplasia]
The
dentin
dysplasias
(
DD
)
,
which
may
be
classified
as
type
1
(
DD
1
)
or
type
2
(
DD
2
)
,
form
a
group
of
rare
,
inherited
dentin
abnormalities
that
are
clinically
distinct
from
dentinogenesis
imperfecta
.
Studies
of
affected
families
may
help
to
distinguish
different
types
of
DD
and
provide
further
insight
into
their
etiology
and
clinical
management
.
This
report
describes
a
family
that
showed
characteristic
dental
features
of
DD
1
,
including
clinically
normal
crowns
in
both
primary
and
permanent
dentitions
,
and
mobile
teeth
that
may
be
associated
with
premature
exfoliation
.
Radiographic
features
included
calcification
of
the
pulp
with
crescent-shaped
,
radiolucent
pulp
remnants
,
short
,
tapering
,
taurodontic
roots
,
and
many
periapical
pathoses
that
may
be
cysts
or
granulomas
.
A
spectrum
of
dentin
dysplasia
was
noted
within
the
family
.
Strategies
to
prevent
pulp
and
periapical
infections
and
early
exfoliation
of
the
teeth
include
meticulous
oral
hygiene
and
effective
caries
-preventive
measures
.
Diseases
Validation
Diseases presenting
"dentinogenesis imperfecta"
symptom
dentin dysplasia
dentinogenesis imperfecta
oligodontia
papillon-lefèvre syndrome
This symptom has already been validated