Dentin dysplasia, type II: report of 2 new families and review of the literature.

[dentin dysplasia]

Dentin dysplasia , type II , is an inherited autosomal dominant disorder in which primary teeth are amber and translucent , with pulp chambers obliterated by abnormal dentin . The permanent teeth have a normal coronal morphologic character and coloration but exhibit "thistle tube "-shaped pulp chambers as well as numerous pulpal calcifications . The disorder has traditionally been thought to be somewhat rare ; however , this article presents 2 new families in which several generations with the disorder were reported to the authors within a 1 -year period . It also includes a review of the literature documenting a total of 17 previously reported families .