Typical radiographic findings of dentin dysplasia type 1b with dental fluorosis.

[dentin dysplasia]

Dentin dysplasia is a rare inherited autosomal dominant disorder characterized by rootless teeth . We hereby report a case of dentin dysplasia type 1 b with typical radiographic findings : short and blunt roots , pulpal obliteration , horizontal /crescent shaped radiolucencies in pulp chambers , and multiple periapical radiolucencies . However , the present case did not show the autosomal dominant pattern of inheritance and the patient also exhibited concurrent dental fluorosis , transposition of 13 and 14 , and multiple cusps in maxillary first molars . Moreover , on careful review of previously documented cases of radiographs of dentin dysplasia , the horizontal /crescent shaped radiolucencies in pulp chambers are a rare finding , which is characteristically seen in the present case .