Coats disease in a 3-week-old boy.

[coats disease]

Coats disease is a rare , idiopathic retinal vasculopathy that predominantly affects males in the first decade of life . We report the case of a 3 -week -old boy who presented with atypical rapidly progressing disease suggestive of Coats exudative vasculopathy . The eye developed retinal fibrosis and phthisis bulbi within 4 weeks . Retinoblastoma could not be ruled out , although histopathology after enucleation revealed no retinoblastoma . To our knowledge , this is the youngest case of Coats disease to be reported in the literature . This case highlights the wide variation in the clinical presentation of Coats disease and the difficulty in differentiating it from diffuse infiltrative retinoblastoma .