Rare Diseases Symptoms Automatic Extraction
Home
A random Abstract
Our Project
Our Team
Benign recurrent intrahepatic cholestasis. Some reflections on a case followed for 20 years.
[benign recurrent intrahepatic cholestasis]
Benign
recurrent
intrahepatic
cholestasis
(
BRIC
)
is
a
form
of
cholestasis
of
obscure
aetiology
characterized
by
recurrent
episodes
of
jaundice
and
itching
associated
with
a
morphological
picture
of
pure
intrahepatic
cholestasis
.
No
effective
treatment
has
yet
been
found
among
the
many
that
have
been
proposed
and
the
invariably
benign
nature
of
the
condition
has
been
questioned
.
A
case
of
BRIC
followed
for
a
period
of
20
years
is
described
.
This
case
is
of
great
interest
from
these
two
points
of
view
:
1
)
the
histologic
and
electron
microscopic
findings
23
and
41
years
after
the
first
episode
of
cholestasis
,
respectively
,
failed
to
reveal
evidence
of
the
possible
future
development
of
cirrhosis
;
2
)
treatment
with
ursodeoxycholic
acid
proved
ineffective
both
therapeutically
and
in
the
prevention
of
episodes
of
bile
stasis
:
on
the
contrary
,
calculosis
of
the
common
bile
duct
appeared
after
8
months
from
the
onset
of
the
treatment
.
Diseases
Validation
Diseases presenting
"respectively"
symptom
adrenal incidentaloma
allergic bronchopulmonary aspergillosis
alpha-thalassemia
benign recurrent intrahepatic cholestasis
carcinoma of the gallbladder
congenital adrenal hyperplasia
congenital diaphragmatic hernia
congenital toxoplasmosis
cushing syndrome
cystinuria
dedifferentiated liposarcoma
dentin dysplasia
dentinogenesis imperfecta
epidermolysis bullosa simplex
esophageal squamous cell carcinoma
familial hypocalciuric hypercalcemia
harlequin ichthyosis
hereditary cerebral hemorrhage with amyloidosis
hirschsprung disease
hodgkin lymphoma, classical
holt-oram syndrome
kallmann syndrome
lamellar ichthyosis
liposarcoma
neonatal adrenoleukodystrophy
neuralgic amyotrophy
oculocutaneous albinism
oligodontia
oral submucous fibrosis
pendred syndrome
pleomorphic liposarcoma
primary effusion lymphoma
proteus syndrome
pyruvate dehydrogenase deficiency
scrub typhus
triple a syndrome
von hippel-lindau disease
well-differentiated liposarcoma
wolf-hirschhorn syndrome
You can validate or delete this automatically detected symptom
Validate the Symptom
Delete the Symptom
