[Recurrent benign intrahepatic cholestasis and their progression to familiar progressive intrahepatic cholestasis].

[benign recurrent intrahepatic cholestasis]

Benign recurrent intrahepatic cholestasis (BRIC ) is a rare form of intrahepatic cholestasis characterized by repeated self-limited episodes of severe pruritus and jaundice . Classically its natural evolution is benign , without progress to fibrosis or hepatic insufficiency ; although , lastly were reported cases which progress to Progressive familial intrahepatic cholestasis (PFIC ). This disease is characterized by progressive hepatic insufficiency and cirrhosis . We present the case of a 32 years old male patient who went to Gastroenterology Service of Arzobispo Loayza National Hospital by pruritus and jaundice . We reported this case for its infrequent presentation and because is an entity which should be considered within differential diagnosis of hepatic cholestasis diseases .

Diseases
Validation

Diseases presenting "intrahepatic cholestasis" symptom

benign recurrent intrahepatic cholestasis

zellweger syndrome

This symptom has already been validated