Rare Diseases Symptoms Automatic Extraction
Home
A random Abstract
Our Project
Our Team
A case report: nasobiliary drainage inducing remission in benign recurrent intrahepatic cholestasis.
[benign recurrent intrahepatic cholestasis]
Benign
recurrent
intrahepatic
cholestasis
is
a
rare
hereditary
disorder
characterized
by
recurrent
episodes
of
cholestasis
and
pruritus
without
anatomical
obstruction
.
Generally
,
medical
therapy
is
not
effective
in
benign
recurrent
intrahepatic
cholestasis
.
Here
,
we
report
the
case
of
a
young
male
patient
with
benign
recurrent
intrahepatic
cholestasis
who
presented
with
cholestatic
jaundice
and
pruritus
,
refractory
to
standard
therapies
.
He
improved
on
treatment
with
temporary
endoscopic
nasobiliary
drainage
.
We
propose
that
temporary
endoscopic
nasobiliary
drainage
should
be
considered
in
cholestatic
benign
recurrent
intrahepatic
cholestasis
patients
.
A
36
-
year
-old
male
patient
admitted
to
our
outpatient
clinic
with
the
complaint
of
pruritus
.
His
anamnesis
revealed
that
he
experienced
the
same
symptoms
and
signs
in
2006
.
He
was
hospitalized
in
a
hepatology
clinic
and
was
thoroughly
examined
.
Liver
biopsy
was
performed
,
and
he
was
finally
diagnosed
as
having
benign
recurrent
intrahepatic
cholestasis
.
Medical
therapy
options
all
proved
to
be
ineffective
and
we
were
able
to
achieve
remission
in
this
patient
only
with
the
help
of
nasobiliary
drainage
.
For
this
patient
,
we
tried
nasobiliary
drainage
in
addition
to
the
standard
medical
therapies
.
He
improved
on
nasobiliary
drainage
.
In
conclusion
,
we
propose
that
temporary
endoscopic
biliary
drainage
should
be
considered
in
cholestatic
benign
recurrent
intrahepatic
cholestasis
patients
.
We
hope
that
this
case
report
contributes
to
the
topic
,
since
only
a
few
nasobiliary
drainage
case
experiences
have
been
reported
to
date
.